先天性眼眶恶性横纹肌样瘤。

Congenital malignant rhabdoid tumor of the orbit.

作者信息

Stidham D B, Burgett R A, Davis M M, Plager D A

机构信息

Indiana University School of Medicine, Department of Ophthalmology, Indianapolis, USA.

出版信息

J AAPOS. 1999 Oct;3(5):318-20. doi: 10.1016/s1091-8531(99)70031-5.

DOI:10.1016/s1091-8531(99)70031-5

PMID:10532580

Abstract

Malignant rhabdoid tumor is a rare and highly malignant renal tumor of infancy. Extrarenal tumors involving the orbit have been reported, but never at birth. The authors describe a primary malignant rhabdoid tumor of the orbit in a neonate who had massive unilateral proptosis at birth. Clinical, radiographic, and histologic features of the tumor are discussed.

摘要

恶性横纹肌样瘤是一种罕见的、高度恶性的婴儿期肾肿瘤。曾有肾外肿瘤累及眼眶的报道，但从未有过出生时即发病的情况。作者描述了一名新生儿眼眶原发性恶性横纹肌样瘤，该患儿出生时即出现单侧眼球大量突出。本文讨论了该肿瘤的临床、影像学和组织学特征。