马凡氏综合征：综述
Marfan's syndrome: a review.
作者信息
Aburawi E H, O'Sullivan J, Hasan A
机构信息
Department of Paediatric Cardiology, Freeman Hospital, Newcastle upon Tyne NE7 7DN.
出版信息
Hosp Med. 2001 Mar;62(3):153-7. doi: 10.12968/hosp.2001.62.3.1535.
PMID:11291465
Abstract
Marfan's syndrome is an inherited disorder of connective tissue, in which the most pronounced abnormalities occur in the musculoskeletal, cardiovascular and ocular systems. Aortic dilatation and dissection are the major causes of morbidity and mortality. Recent advances in surgical techniques and earlier intervention have reduced postoperative mortality and morbidity.
摘要
马凡氏综合征是一种遗传性结缔组织疾病，其中最明显的异常发生在肌肉骨骼、心血管和眼部系统。主动脉扩张和夹层是发病和死亡的主要原因。手术技术的最新进展和早期干预降低了术后死亡率和发病率。
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