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[结节病相关的血管炎和胶原血管受累]

[Vasculitis and collagenous-vascular involvement in association with sarcoidosis].

作者信息

Ooi Hidemi, Suzuki Eiichi

机构信息

Division of Respiratory Medicine, Niigata University Graduate School of Medical and Dental Sciences.

出版信息

Nihon Rinsho. 2002 Sep;60(9):1772-7.

Abstract

Sarcoidosis is a systemic granulomatous disorder of unknown origin. It unusually complicates systemic vascular involvement. We concisely review clinico-pathological findings of vascular involvement, including granulomatous angitis and microangiopathy. The clinical features of sarcoidosis may mimic those of many rheumatic disorders and sarcoidosis may coexist with autoimmune diseases. We review both rheumatologic manifestations, including bone, joint, and muscle of sarcoidosis and immunological findings of autoimmune diseases complicated with sarcoidosis, including 2-case reports of Sjögren's syndrome and dermatomyositis/polymyositis.

摘要

结节病是一种病因不明的全身性肉芽肿性疾病。它罕见地合并全身性血管受累。我们简要回顾血管受累的临床病理表现,包括肉芽肿性血管炎和微血管病变。结节病的临床特征可能与许多风湿性疾病相似,且结节病可能与自身免疫性疾病共存。我们回顾了结节病的风湿性表现,包括骨骼、关节和肌肉方面,以及合并结节病的自身免疫性疾病的免疫学表现,包括2例干燥综合征和皮肌炎/多发性肌炎的病例报告。

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