Paolini Sergio, Ciappetta Pasquale, Domenicucci Maurizio, Guiducci Antonio
Department of Neurological Sciences and Neurosurgery, Ospedale Santa Maria, Terni, Italy.
Neurosurgery. 2003 Jan;52(1):243-5; discussion 246. doi: 10.1097/00006123-200301000-00033.
Spinal neurenteric cysts are rare congenital lesions that may occur either alone or in the context of a complex malformative disorder including typical vertebral and cutaneous abnormalities. The interest of the case of a spinal neurenteric cyst described here lies in its rare intramedullary location and in the false mural nodule image on the preoperative magnetic resonance imaging scan. A further distinctive feature is the association with a cleft spinal cord.
A 28-year-old woman presented with a 2-year history of progressive paraparesis and urinary retention. A magnetic resonance imaging study disclosed a T8-T9 intramedullary cystic lesion with a mural nodulelike formation on the posterior face.
A posterior midline myelotomy exposed a cystic lesion that had translucent walls and contained a milky fluid. No mural nodules were found. Once the cyst had been emptied, a collateral finding was a cleft that was clearly observed in the anterior spinal cord. The histological diagnosis was a neurenteric cyst. Retrospectively, the nodular lesion found on the preoperative scan was attributed to mucinous clots deposited at the bottom of the cyst.
This case report demonstrates that neurenteric cysts can vary widely in radiological appearance, depending on the contents of the cyst. These differences become especially important if the associated stigmata are lacking and the preoperative diagnosis rests on magnetic resonance imaging scan appearance alone.
脊髓神经管囊肿是一种罕见的先天性病变,可单独出现,也可在包括典型脊柱和皮肤异常的复杂畸形疾病背景下发生。此处描述的脊髓神经管囊肿病例的有趣之处在于其罕见的髓内位置以及术前磁共振成像扫描上的假壁结节影像。另一个显著特征是与脊髓纵裂相关。
一名28岁女性,有2年进行性双下肢轻瘫和尿潴留病史。磁共振成像检查发现T8 - T9节段髓内囊性病变,后壁有壁结节样结构。
后正中脊髓切开术暴露了一个囊性病变,其壁半透明,内含乳白色液体。未发现壁结节。囊肿排空后,一个附带发现是在前脊髓中清晰可见的裂隙。组织学诊断为神经管囊肿。回顾性分析,术前扫描发现的结节性病变归因于沉积在囊肿底部的黏液性凝块。
本病例报告表明,神经管囊肿的放射学表现可能因囊肿内容物不同而有很大差异。如果缺乏相关体征且术前诊断仅基于磁共振成像扫描表现,这些差异就显得尤为重要。