Alehan Dursun, Hallioglu Olgu
Division of Pediatric Cardiology, Department of Pediatrics, Hacettepe University Faculty of Medicine, Ankara, Turkey.
J Am Soc Echocardiogr. 2003 Jan;16(1):91-3. doi: 10.1067/mje.2003.26.
Double outlet left ventricle (DOLV) is a rare congenital cardiac malformation in which both the pulmonary artery and the aorta arise exclusively or predominantly from the morphologic left ventricle. We describe a case of DOLV with situs solitus, d-loop ventricles, d-malposition of the great arteries (S, D, D), severe pulmonary stenosis, and a subaortic ventricular septal defect in which the left ventricle was also severely hypoplastic. The anatomic features were shown with 2-dimensional echocardiography, and the diagnosis was later confirmed at cardiac catheterization. Many morphologic variations of this malformation have been described but to the our knowledge DOLV with a hypoplastic left ventricle has not been reported before.
双出口左心室（DOLV）是一种罕见的先天性心脏畸形，其中肺动脉和主动脉完全或主要起源于形态学上的左心室。我们描述了一例具有正常心脏位置、d型心室、大动脉d型转位（S，D，D）、严重肺动脉狭窄和主动脉下室间隔缺损的DOLV病例，该病例中的左心室也严重发育不全。二维超声心动图显示了解剖特征，随后通过心导管检查确诊。已经描述了这种畸形的许多形态学变异，但据我们所知，以前尚未报道过左心室发育不全的DOLV。
