Köhler U
Universitäts-Augenklinik Marburg a.d. Lahn.
Ophthalmologica. 1992;205(3):158-62. doi: 10.1159/000310333.
The clinical features of Posner-Schlossman syndrome and the various differential diagnoses are described in a 20-year-old patient. Additional to Posner-Schlossman syndrome this patient showed signs of Axenfeld's anomaly. He also presented symptoms of a status-dysrhaphicus-like state after atrial septal defect and the ability to overstrain the distal finger joints. Posner-Schlossman syndrome, heterochromic cyclitis, anterior-chamber cleavage syndrome and ICE syndrome (iridocorneal-endothelial syndrome: Chandler's, Cogan-Reese syndrome and progressive essential iris atrophy) often produce similar effects at the Descemet membrane, the anterior chamber angle and the iris. Because of the same mesodermal origin of these tissues we suggest that all the diseases mentioned above are merely different clinical expressions of one main disease.
一名20岁患者的波斯纳-施洛斯曼综合征的临床特征及各种鉴别诊断情况被予以描述。除了波斯纳-施洛斯曼综合征外,该患者还表现出阿克森费尔德异常的体征。他还出现了房间隔缺损后类发育异常状态的症状以及远端指关节过度伸展的能力。波斯纳-施洛斯曼综合征、异色性睫状体炎、前房劈裂综合征和ICE综合征(虹膜角膜内皮综合征:钱德勒综合征、科根-里斯综合征和进行性原发性虹膜萎缩)常在Descemet膜、前房角和虹膜处产生相似影响。由于这些组织具有相同的中胚层起源,我们认为上述所有疾病仅仅是一种主要疾病的不同临床表型。