Jha Sanjeev, Patel R
Department of Neurology, Sanjay Gandhi Post Graduate Institute of Medical Sciences, Raebareli Road, Lucknow 226014, India.
Neurol India. 2004 Sep;52(3):369-71.
The Kluver-Bucy syndrome (KBS) is a neurobehavioral syndrome and can be seen in association with a variety of neurological disorders. Case records of 6 patients with KBS seen during a period of 5 years in a university hospital were reviewed. During the study period 6 patients with KBS, aged between 4 and 14 years, were seen. Hyperorality, hypersexuality, and abnormal behavior were the most common manifestations. Of the 6 patients, 5 had recurrent unprovoked seizures. The associated neurological disorders included anoxia-ischemic encephalopthy (2), herpes simplex encephalitis (1), neurocysticercosis (NCC) (1), traumatic brain injury with gliosis (1 case) and tuberculous meningitis (1 case). Prognosis was poor in all the patients except in the patient with NCC.
克吕弗-布西综合征(KBS)是一种神经行为综合征,可见于多种神经系统疾病。回顾了一所大学医院5年间收治的6例KBS患者的病例记录。在研究期间,共诊治了6例年龄在4至14岁之间的KBS患者。口欲亢进、性欲亢进和异常行为是最常见的表现。6例患者中,5例有无诱因的反复发作性癫痫。相关的神经系统疾病包括缺氧缺血性脑病(2例)、单纯疱疹性脑炎(1例)、神经囊尾蚴病(NCC)(1例)、伴有胶质增生的创伤性脑损伤(1例)和结核性脑膜炎(1例)。除NCC患者外,所有患者的预后均较差。