Bosdure E, Mates M, Mely L, Guys J M, Devred P, Dubus J C
Unité de médecine infantile, CHU Timone-Enfants, 13385 Marseille cedex 05, France.
Arch Pediatr. 2005 Feb;12(2):168-72. doi: 10.1016/j.arcped.2004.11.012.
Hemolymphangioma is a benign malformation of the lymphatic vessels. Cervical localisation is the most frequent. Mediastinal localisation is rare, but may be life-threatening because of airway compression. We report on a four-month-old boy who presented, in a context of epidemics, with clinical signs of acute bronchiolitis requiring mechanical ventilation for several days. Chest X-rays showed an important mediastinal mass with airways compression. Diagnosis was evoked on CT-scan aspects and confirmed by histology. Surgery allowed complete resolution, but dysphonia and oropharyngeal disorders persisted for several months. This rare congenital malformation is reviewed.
血淋巴管瘤是淋巴管的一种良性畸形。颈部是最常见的发病部位。纵隔发病较为罕见,但由于气道受压可能危及生命。我们报告了一名4个月大的男婴,在疫情期间出现急性细支气管炎的临床症状,需要机械通气数日。胸部X光片显示纵隔有一个巨大肿块并伴有气道受压。根据CT扫描结果怀疑诊断,并经组织学证实。手术使病情完全缓解,但声音嘶哑和口咽疾病持续了数月。本文对这种罕见的先天性畸形进行了综述。