Daccarett Marcos, Burke Peter, Saba Souheil
Division of Cardiology, Providence Hospital and Medical Center, 16001 W. 9 Mile Road, Southfield, MI 48075, USA.
Eur J Echocardiogr. 2006 Jun;7(3):253-6. doi: 10.1016/j.euje.2005.04.008. Epub 2005 May 31.
Papillary fibroelastoma (PFE) is an uncommon primary neoplasm of cardiac origin. They are solitary neoplasms that historically were an incidental finding at the time of autopsy. With the advent of two-dimensional echocardiography, symptomatic cases have been reported in current literature, thus causing a paradigm shift in the management of these tumors. Although the majority of PFE are benign, because of their potential risk for complication related to embolic and obstructive phenomena, they are now considered hazardous and require tumor excision even in asymptomatic patients. We report a case of an asymptomatic incidental large papillary fibroelastoma within the right ventricular outflow tract.
乳头状纤维弹性瘤(PFE)是一种罕见的起源于心脏的原发性肿瘤。它们是孤立性肿瘤,在过去尸检时多为偶然发现。随着二维超声心动图的出现,目前文献中已有有症状病例的报道,这使得这些肿瘤的治疗模式发生了转变。尽管大多数PFE是良性的,但由于它们存在与栓塞和阻塞现象相关的潜在并发症风险,现在被认为具有危险性,即使是无症状患者也需要切除肿瘤。我们报告一例右心室流出道无症状偶然发现的巨大乳头状纤维弹性瘤病例。