20年后肺血管内支气管肺泡瘤复发并伴有纵隔转移。

Recurrence of pulmonary intravascular bronchoalveolar tumor with mediastinal metastasis 20 years later.

作者信息

Chen Tze-Ming, Donington Jessica, Mak Gordon, Berry Gerald J, Ruoss Stephen J, Rosen Glenn D, Upadhyay Daya

机构信息

Division of Pulmonary and Critical Care Medicine, Stanford University Medical Center, 300 Pasteur Drive, Room H3143, Stanford, CA 94305-5236, USA.

出版信息

Respir Med. 2006 Feb;100(2):367-70. doi: 10.1016/j.rmed.2005.05.010. Epub 2005 Jun 28.

DOI:10.1016/j.rmed.2005.05.010

PMID:15990286

Abstract

Pulmonary intravascular bronchoalveolar tumor (IVBAT) also recognized as pulmonary epithelioid hemangioendothelioma, is a rare malignant vascular tumor of unknown etiology. IVBAT is a tumor of multicentric origin and the lungs are rarely involved, with only about 60 cases of pulmonary IVBAT described in the literature. The prognosis is unpredictable, with life expectancy ranging from 1 to 15 years. We report an unusual case of pulmonary IVBAT that recurred in the lung with metastasis to the mediastinum.

摘要

肺血管内支气管肺泡瘤（IVBAT）也被认为是肺上皮样血管内皮瘤，是一种病因不明的罕见恶性血管肿瘤。IVBAT是一种多中心起源的肿瘤，肺部很少受累，文献中仅描述了约60例肺IVBAT病例。其预后难以预测，预期寿命为1至15年。我们报告了一例不寻常的肺IVBAT病例，该病例在肺部复发并转移至纵隔。