Valle Laura, Fernández Victoria, Pérez-Pons Concepción, Sánchez Félix García, Benítez Javier, Urioste Miguel
Familial Cancer Unit, Human Cancer Genetics Program, Centro Nacional de Investigaciones Oncológicas, Madrid, Spain.
Hematol Oncol. 2006 Jun;24(2):86-8. doi: 10.1002/hon.775.
This report describes a chronic myelogenous leukaemia patient with an apparently normal bone marrow karyotype but BCR/ABL fusion-gene-positive. Commercial FISH probes showed an atypical pattern and the BCR/ABL fusion transcript was detected by RT-PCR, but not the reciprocal ABL/BCR. Consecutive FISH assays clarified the mechanism of the masked Ph. The ABL gene and the following 5.6-5.7 Mb of 9q are inserted into the BCR region of chromosome 22. There is no transference of 22q material to chromosome 9 or to any other chromosomes. Clinical features and evolution of the patient are similar to those cases with classic Ph chromosome.
本报告描述了一名慢性粒细胞白血病患者,其骨髓核型看似正常,但BCR/ABL融合基因呈阳性。商业荧光原位杂交(FISH)探针显示出非典型模式,通过逆转录聚合酶链反应(RT-PCR)检测到了BCR/ABL融合转录本,但未检测到反向的ABL/BCR。连续的FISH检测阐明了隐匿性费城染色体(Ph)的机制。ABL基因以及9号染色体长臂9q接下来的5.6 - 5.7兆碱基对插入到了22号染色体的BCR区域。没有22号染色体长臂物质转移到9号染色体或任何其他染色体。该患者的临床特征和病情演变与经典Ph染色体病例相似。