Rasković S, Bogić M, Perić-Popadić A, Tomić-Spirić V
Srp Arh Celok Lek. 1997 Jan-Feb;125(1-2):54-8.
Sjogren's syndrome is a chronic inflammatory disease of unknown aethiology. It is characterized by decreased secretion of salivary and lacrimal glands, which induces keratoconjunctivitis sicca and xerostomia. Sjogren's syndrome is a central autoimmune disease, and it has characteristics of both organ-specific and generalized autoimmune diseases. It can exist as a primary disease or is associated with other autoimmune diseases (most freyuently with systemic lupus erythematosus or rheumatoid arthritis) and is classified as a secondary Sjogren's syndrome. The aethiology is multifactorial, and it has not yet been completely explained. In the pathogenesis of the disease the important role have genetic predisposition, chronic oestrogen stimulation, end viral infections, especially of the herpes virus group (EBV, CMV, HHV6) and retroviruses. In the clinical picture xerostomia, xerophtalmia and non-erosive arthritis are the most common features, with the whole spectrum of extraglandular manifestations of respiratory, gastrointestinal, skin, and haematologic, neurologic and endocrinologic disturbances. Pathohistological findings of minor labial salivary gland lymphocyte infiltration is the most specific and the most sensitive diagnostic criterion of Sjogren's syndrome. The diagnosis of keratoconjunctivitis sicca is made by Schrimer's test, Rose bengal dye staining and by the "tear break up time". Differential diagnosis of Sjogren's syndrome includes an extremely large number of various pathologic states. The treatment of Sjogren's syndrome consists of symptomatic treatment of dry mucosas (artificial tears, etc.) and also of antiinflammatory drugs, glucocorticoids, immunosuppressive drugs. Plasmapheresis and intravenous administration of immunoglobulins are used for immunosuppression in these patients.
干燥综合征是一种病因不明的慢性炎症性疾病。其特征是唾液腺和泪腺分泌减少,从而导致干燥性角结膜炎和口干症。干燥综合征是一种中枢性自身免疫性疾病,具有器官特异性自身免疫疾病和全身性自身免疫疾病的特征。它可以作为原发性疾病存在,也可与其他自身免疫性疾病相关(最常见的是系统性红斑狼疮或类风湿性关节炎),并被归类为继发性干燥综合征。病因是多因素的,尚未完全阐明。在该疾病的发病机制中,遗传易感性、慢性雌激素刺激、病毒感染尤其是疱疹病毒组(EBV、CMV、HHV6)和逆转录病毒起重要作用。在临床表现中,口干、眼干和非侵蚀性关节炎是最常见的特征,还伴有呼吸、胃肠、皮肤、血液、神经和内分泌系统紊乱等一系列腺外表现。唇腺小唾液腺淋巴细胞浸润的病理组织学发现是干燥综合征最具特异性和最敏感的诊断标准。干燥性角结膜炎的诊断通过施密特试验、孟加拉玫瑰红染色和“泪膜破裂时间”来进行。干燥综合征的鉴别诊断包括大量不同的病理状态。干燥综合征的治疗包括对干燥黏膜的对症治疗(人工泪液等)以及抗炎药物、糖皮质激素、免疫抑制药物。血浆置换和静脉注射免疫球蛋白用于这些患者的免疫抑制治疗。