[臂丛双瘫作为肌萎缩侧索硬化症的一种变体（维尔皮安 - 伯恩哈特综合征）：墨西哥首例报告病例及文献综述]
[Brachial diplegia as a variant of amyotrophic lateral sclerosis (Vulpian-Bernhart syndrome): the first case reported in Mexico and a review of the literature].
作者信息
San-juan O D, Castro-Macías J I, Cárdenas-Hernández G
机构信息
Departamento de Neurología, Instituto Nacional de Neurología, México DF, México.
出版信息
Rev Neurol. 2008;46(1):30-1.
INTRODUCTION
Brachial diplegia refers to an atypical clinical variant of amyotrophic lateral sclerosis (ALS), which is defined as a lower motor neuron disease in the upper limbs, with no significant functional complications in other regions.
CASE REPORT
A 65-year-old female who presented a clinical picture of brachial diplegia that slowly progressed over a period of 72 months. Neurophysiology studies revealed a chronic denervation process. Throughout a follow-up lasting one year the clinical course remained stable.
CONCLUSIONS
Brachial diplegia in females is a rare form of presentation of ALS and they probably have a higher survival rate than males.
引言
臂丛性双侧瘫指肌萎缩侧索硬化症（ALS）的一种非典型临床变体，其被定义为上肢的下运动神经元疾病，其他部位无明显功能并发症。
病例报告
一名65岁女性呈现出臂丛性双侧瘫的临床表现，该症状在72个月内缓慢进展。神经生理学研究显示存在慢性去神经支配过程。在为期一年的随访中，临床病程保持稳定。
结论
女性臂丛性双侧瘫是ALS的一种罕见表现形式，且她们的生存率可能高于男性。
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