朗格汉斯细胞组织细胞增多症：胸腺内支气管源性囊肿与胸腺囊肿并存。

Langerhans cell histiocytosis: coexistence of bronchogenic and thymic cysts in the thymus.

作者信息

Kawano Ryoji, Hata Enjo, Ikeda Shingo, Yokota Toshiya, Tagawa Kohei, Sato Fumitomo

机构信息

Surgical Department of Respiratory Center, Mitsui Memorial Hospital, Kandaizumicho-1, Chiyoda-ku, Tokyo 101-8643, Japan.

出版信息

Gen Thorac Cardiovasc Surg. 2008 Feb;56(2):74-6. doi: 10.1007/s11748-007-0191-x. Epub 2008 Feb 24.

DOI:10.1007/s11748-007-0191-x

PMID:18297462

Abstract

Langerhans cell histiocytosis (LCH) is a disease caused by the proliferation of Langerhans cells in various tissues or organs. A 43-year-old male patient presented with an anterior mediastinal mass in the thymus. Histological examination after a thymectomy revealed a bronchogenic cyst in the thymus, and multiple LCH and small thymic cysts were also incidentally observed in the thymus. Unifocal LCH in an adult occurring in the thymus is extremely rare. Furthermore, no cases of LCH with the coexistence of bronchogenic and thymic cysts in the thymus have been previously reported.

摘要

朗格汉斯细胞组织细胞增多症（LCH）是一种由朗格汉斯细胞在各种组织或器官中增殖引起的疾病。一名43岁男性患者出现胸腺前纵隔肿块。胸腺切除术后的组织学检查显示胸腺中有一个支气管源性囊肿，同时在胸腺中还偶然发现了多个朗格汉斯细胞组织细胞增多症病灶和小的胸腺囊肿。成人胸腺中发生的单灶性朗格汉斯细胞组织细胞增多症极为罕见。此外，此前尚无胸腺中同时存在支气管源性囊肿和胸腺囊肿的朗格汉斯细胞组织细胞增多症病例的报道。