[CT findings of thorax and abdominopelvic with pulmonary lymphangiomyomatosis].

OBJECTIVE

To investigate the CT findings of thorax and abdominopelvic with pulmonary lymphangiomyomatosis.

METHOD

The clinical data, CT findings, and histopathological data of 14 patients with pulmonary lymphangiomyomatosis were analyzed.

RESULTS

Typical high resolution CT (HRCT) findings of 14 patients with pulmonary lymphangiomyomatosis were diffusely scattered with small imperceptible-walled or thin-walled cysts (diameter < 1 cm) throughout both lungs. Other findings in thorax included: small noncalcified pulmonary nodules in 1 case, bilateral patchy shadows in 1 case, subpleural bulla in 3 cases, honeycombing sign in 1 case, mediastinal lymphadenopathy in 2 cases, pericardial effusion in 1 case, and pleural effusion in 3 cases. Nine patients had abnormal abdominopelvic findings: renal and hepatic angiomyolipoma in 1 case, retroperitoneal lymphangioleiomyoma in 6 cases, retroperitoneal lymphadenopathy in 1 case, and uterine leiomyoma in 1 case.

CONCLUSION

Pulmonary lymphangiomyomatosis has typical pectoral CT findings. It is also often accompanied with abdominopelvic abnormity with typical CT findings.