Kelly Robert E
Department of Surgery, Children's Hospital of The King's Daughters, Eastern Virginia Medical School, 601 Children's Lane, Suite 5B, Norfolk, VA 23507, USA.
Semin Pediatr Surg. 2008 Aug;17(3):181-93. doi: 10.1053/j.sempedsurg.2008.03.002.
Pectus excavatum is a depression of the sternum and costal cartilages which may present at birth, or more commonly during the teenage growth spurt. Symptoms of lack of endurance, shortness of breath with exercise, or chest pain are frequent. Although pectus excavatum may be a component of some uncommon syndromes, patients usually are healthy. Evaluation should include careful anatomic description with photographs, radiography to demonstrate the depth of the depression, extent of cardiac compression, or displacement, measurement of pulmonary function, and echocardiography to look for mitral valve prolapse (in 15%) or diminished right ventricular volume. Indications for surgical treatment include two or more of the following: a severe, symptomatic deformity; progression of deformity; paradoxical respiratory chest wall motion; computer tomography scan with a pectus index greater than 3.25; cardiac compression/displacement and/or pulmonary compression; pulmonary function studies showing restrictive disease; mitral valve prolapse, bundle branch block, or other cardiac pathology secondary to compression of the heart; or failed previous repair(s). The developmental factors, genetics, and physiologic abnormalities associated with the condition are reviewed.
漏斗胸是指胸骨和肋软骨凹陷,可能在出生时就出现,更常见于青少年生长突增期。耐力缺乏、运动时呼吸急促或胸痛等症状很常见。尽管漏斗胸可能是某些罕见综合征的一部分,但患者通常身体健康。评估应包括通过照片进行仔细的解剖学描述、进行放射照相以显示凹陷深度、心脏受压或移位的程度、测量肺功能以及进行超声心动图检查以寻找二尖瓣脱垂(15%的患者)或右心室容积减小。手术治疗的指征包括以下两项或更多:严重的症状性畸形;畸形进展;矛盾性呼吸胸壁运动;计算机断层扫描显示漏斗胸指数大于3.25;心脏受压/移位和/或肺部受压;肺功能研究显示限制性疾病;二尖瓣脱垂、束支传导阻滞或其他因心脏受压继发的心脏病变;或既往修复失败。本文回顾了与该病症相关的发育因素、遗传学和生理异常情况。