Smith Julie J L, Oliver G Fergus
Department of Medicine, Waitemata District Health Board, Auckland, New Zealand.
J Am Acad Dermatol. 2009 Jan;60(1):149-52. doi: 10.1016/j.jaad.2008.07.036.
Febrile ulceronecrotic Mucha-Habermann disease is a rare severe variant of pityriasis lichenoides et varioliformis acuta, a disease within the pityriasis lichenoides spectrum of disorders. It remains uncertain whether these disorders are preneoplastic or reactive against infectious or other antigenic stimuli. Febrile ulceronecrotic Mucha-Habermann disease varies in severity and may be accompanied by a range of systemic symptoms. We present a case associated with herpes simplex virus infection. In this case, no significant T cell clone was identified. Clonality may be a prognostic marker, but reports with T-cell receptor polymerase chain reaction results are limited to eight previous cases, and further reports are required. Awareness of the condition is important because of its fulminant potential.
发热性溃疡性坏死性穆查-哈伯曼病是急性痘疮样苔藓样糠疹的一种罕见严重变型,急性痘疮样苔藓样糠疹是苔藓样糠疹谱系疾病中的一种。这些疾病是肿瘤前期病变还是对感染性或其他抗原性刺激的反应仍不确定。发热性溃疡性坏死性穆查-哈伯曼病严重程度各异,可能伴有一系列全身症状。我们报告一例与单纯疱疹病毒感染相关的病例。在该病例中,未发现明显的T细胞克隆。克隆性可能是一种预后标志物,但T细胞受体聚合酶链反应结果的报告仅限于之前的8例病例,还需要更多报告。鉴于其潜在的暴发性,认识这种疾病很重要。