脱髓鞘性弥漫性硬化（希尔德病）：临床与神经放射学相关性
Myelinoclastic diffuse sclerosis (Schilder's disease): cliniconeuroradiologic correlations.
作者信息
Eblen F, Poremba M, Grodd W, Opitz H, Roggendorf W, Dichgans J
机构信息
Neurologische Universitätsklinik Tübingen, Germany.
出版信息
Neurology. 1991 Apr;41(4):589-91. doi: 10.1212/wnl.41.4.589.
We report a 17-year-old boy with myelinoclastic diffuse sclerosis (Schilder's disease) presenting with left leg paresis, visual loss, and behavioral changes. CT and MRI showed two large lesions in the subcortical white matter of the occipital and parietal lobes of both hemispheres and increased intracranial pressure. Histology disclosed large areas of demyelination and perivascular infiltrates. The patient improved with coincident oral prednisolone treatment.
我们报告了一名17岁患有髓鞘破坏性弥漫性硬化症（席尔德病）的男孩，其表现为左腿轻瘫、视力丧失和行为改变。CT和MRI显示双侧枕叶和顶叶皮质下白质有两个大病灶，颅内压升高。组织学检查发现大片脱髓鞘和血管周围浸润。该患者在同时口服泼尼松龙治疗后病情好转。
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