Tuna Elif B, Orino Daisuke, Ogawa Kei, Yildirim Mine, Seymen Figen, Gencay Koray, Maeda Takahide
Department of Pedodontics, Istanbul University, Istanbul, Turkey.
J Oral Sci. 2011 Mar;53(1):121-4. doi: 10.2334/josnusd.53.121.
We describe the dental and craniofacial anomalies of 2 ethnically distinct patients with Goldenhar syndrome, which is characterized by hemifacial microsomia, facial asymmetry, and ear and dental abnormalities. A 7-year-old Japanese girl and 12-year-old Turkish boy with Goldenhar syndrome were examined clinically and radiographically; both had symptoms of hemifacial microsomia. Multiple organ involvement can limit surgical correction of deformities and affect patient management. Therefore, long-term regular follow-up by a multidisciplinary team is important to monitor the growth and development of patients.
我们描述了两名患有Goldenhar综合征的不同种族患者的牙齿和颅面异常情况,该综合征的特征为半侧颜面短小、面部不对称以及耳部和牙齿异常。对一名7岁的日本女孩和一名12岁的土耳其男孩进行了临床和影像学检查,他们均有半侧颜面短小的症状。多器官受累会限制畸形的手术矫正并影响患者管理。因此,由多学科团队进行长期定期随访对于监测患者的生长发育很重要。