Tostivint L, Pop-Jora D, Grimprel E, Quinet B, Lesprit E
Service de pédiatrie générale, hôpital intercommunal de Créteil, 40, avenue de Verdun, Créteil, France.
Arch Pediatr. 2012 Jun;19(6):612-5. doi: 10.1016/j.arcped.2012.03.016. Epub 2012 Apr 27.
Vaso-occlusive crises are the most common complication of sickle cell disease. Orbital bone infarction is an unusual manifestation of sickling disorders. It is suspected in patients with acute painful periorbital swelling. Orbital compression syndrome with possible optic nerve injury is a rare but serious complication; therefore, this diagnosis should be considered. Orbital infarction can be difficult to distinguish from osteomyelitis or skin infections. Imaging can be helpful in differentiating infection from infarction. We report a case of orbital bone infarction in a 14-year-old boy with sickle cell disease. Under medical treatment, the clinical course resolved with no sequelae.
血管闭塞性危象是镰状细胞病最常见的并发症。眼眶骨梗死是镰状细胞病的一种罕见表现。在急性眶周疼痛性肿胀的患者中应怀疑此病。伴有可能的视神经损伤的眼眶压迫综合征是一种罕见但严重的并发症;因此,应考虑这一诊断。眼眶梗死可能难以与骨髓炎或皮肤感染相区分。影像学检查有助于区分感染与梗死。我们报告一例14岁患镰状细胞病男孩的眼眶骨梗死病例。在接受药物治疗后,临床病程顺利解决,未留下后遗症。