一名患有低纤维蛋白原血症的儿童反复出现玻璃体出血和硬膜外血肿。
Recurrent vitreous haemorrhage and epidural haematoma in a child with hypofibrinogenaemia.
作者信息
Mansour Ahmad M, Jaroudi Mahmoud O
机构信息
Department of Ophthalmology, American University of Beirut, Beirut, Lebanon.
出版信息
BMJ Case Rep. 2012 Jul 9;2012:bcr2012006478. doi: 10.1136/bcr-2012-006478.
A 14-month-old male infant was brought by parents for redness of the right eye of 18 days duration. Exam and B-scan ultrasonography revealed total hyphema, dense vitreous haemorrhage and lens subluxation in the right eye while CT disclosed right small epidural haematoma. The left eye had neither retinal haemorrhage nor disc oedema. There was no sign of shaken baby syndrome. Fibrinogen level in the blood was very low. The parents are first-degree cousins with two family members having hypofibrinogenaemia. Vitreous haemorrhage recurred after surgical intervention resulting in phthisis and loss of vision. Hypofibrinogenaemia needs to be included in the differential diagnosis of ocular haemorrhage and vision loss.
一名14个月大的男婴被父母带到医院，其右眼发红已有18天。检查和B超检查显示右眼有全前房积血、致密玻璃体出血和晶状体半脱位，而CT显示右侧有小的硬膜外血肿。左眼既没有视网膜出血也没有视盘水肿。没有摇晃婴儿综合征的迹象。血液中的纤维蛋白原水平非常低。父母是一级亲属，有两名家庭成员患有低纤维蛋白原血症。手术干预后玻璃体出血复发，导致眼球痨和视力丧失。低纤维蛋白原血症需要列入眼部出血和视力丧失的鉴别诊断中。
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