Department of Thoracic Surgery, Georges Pompidou European Hospital, Descartes University, Paris, France.
Eur J Cardiothorac Surg. 2013 Dec;44(6):1137-9. doi: 10.1093/ejcts/ezt214. Epub 2013 May 3.
We report a rare case of a giant desmoid tumour responsible for cardiac and respiratory failure. Complete removal was decided upon, despite an initial failure in another centre because of symptom severity. In such cases, wide local resection remains the best therapeutic approach, but the risk of local recurrence is high. Literature review confirms the exceptional presentation and the benefit of aggressive surgery.
我们报告了一例罕见的巨大型硬纤维瘤导致心脏和呼吸衰竭的病例。尽管在另一家中心因症状严重而最初手术失败,但仍决定进行完全切除。在这种情况下,广泛局部切除仍然是最佳的治疗方法,但局部复发的风险很高。文献回顾证实了这种罕见的表现以及积极手术的益处。