Bouguila J, Khalef I, BenAli M, Sriha B, Soyah N, Boughammoura L
Service de pédiatrie, CHU Farhat Hached, avenue Ibn El Jazzar, 4000 Sousse, Tunisie.
Rev Stomatol Chir Maxillofac Chir Orale. 2013 Feb;114(1):46-8. doi: 10.1016/j.stomax.2012.07.010. Epub 2012 Nov 22.
A schwannoma is a benign slow growing tumor originating from the peripheral nerve sheath. Its tongue base location is extremely rare, especially in very young patients.
A 15-year-old female patient was admitted in emergency for moderate hematemesis. The clinical examination revealed swelling of the tongue base, causing the bleeding. This lesion had appeared when she was 3years of age and no treatment was done. A complete surgical excision was performed and the histopathological examination allowed diagnosing a tongue base schwannoma. The postoperative outcome was uneventful, and no recurrence was detected 6months after surgery.
The particularities of this report are the patient's very young age and the tumor's tongue base location. The prognosis is usually good after complete excision, if there is only one tumor. Type 2 neurofibromatosis should be excluded, given the risk of malignant degeneration.
施万细胞瘤是一种起源于周围神经鞘的良性生长缓慢的肿瘤。其位于舌根处极为罕见,尤其是在非常年轻的患者中。
一名15岁女性患者因中度呕血急诊入院。临床检查发现舌根肿胀并导致出血。该病变在她3岁时出现,未进行任何治疗。进行了完整的手术切除,组织病理学检查确诊为舌根施万细胞瘤。术后恢复顺利,术后6个月未发现复发。
本报告的特殊之处在于患者非常年轻以及肿瘤位于舌根。如果只有一个肿瘤,完整切除后的预后通常良好。鉴于存在恶性变的风险,应排除2型神经纤维瘤病。