外胚层发育不良所致瘢痕性外耳道狭窄：拉普-霍奇金综合征。
Cicatricial external auditory canal stenosis caused by ectodermal dysplasia: Rapp-Hodgkin syndrome.
作者信息
Sosulski Amanda B, Hayes James D
机构信息
Department of Surgery, Winthrop-University Hospital, Mineola, NY, USA.
出版信息
Ear Nose Throat J. 2013 Jun;92(6):E24. doi: 10.1177/014556131309200617.
We present a case of recurrent cicatricial stenosis of the external ear canals caused by ectodermal dysplasia, specifically Rapp-Hodgkin syndrome, in a 45-year-old woman. No form of medical or surgical management has produced durable patency of the patient's ear canals, and her hearing loss is being managed with hearing aids. Topical management of the recurring external otitis slows the process but has been unsuccessful in preventing restenosis of both external auditory canals.
我们报告了一例45岁女性因外胚层发育不良，具体为拉普-霍奇金综合征导致外耳道复发性瘢痕性狭窄的病例。任何形式的药物或手术治疗都未能使患者的耳道保持持久通畅，她的听力损失通过助听器进行处理。复发性外耳道炎的局部治疗减缓了病情发展，但未能成功预防双侧外耳道再狭窄。
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