Department of Orthopaedic Surgery, Yonsei University College of Medicine, 50 Yonsei-ro, Seodaemun-gu, Seoul 120-752, Korea.
Yonsei Med J. 2014 Jan;55(1):178-84. doi: 10.3349/ymj.2014.55.1.178.
Multiple hereditary exostoses of the forearm typically form in the distal ulna, causing disturbances in the growth of the ulna and functional disability. Multiple hereditary exostoses inhibit the growth of the ulna, leading to an acquisition of a varus deformity in the radius, which sometimes leads to dislocation of the radial head, the development of limitations in the pronation-supination of the forearm, and cosmetic problems.
We retrospectively reviewed the cases of four patients who had deformities of the forearm with radial head dislocation associated with multiple hereditary exostoses, and evaluated the radiologic and clinical results of excision of the osteochondromas from the distal ulna and gradual ulnar lengthening with an Ilizarov external fixator.
Good clinical and radiological results were obtained after a mean follow-up of 25 months. At the most recent follow-up, radial bowing, ulnar shortening, carpal slip, and the pronation/supination arch of the forearm had improved. There was little change in terms of preoperative radial articular angle and the flexion/extension arch of the elbow by the most recent follow-up.
Treatment of four forearms from four patients by excision of osteochondromas and gradual lengthening of the ulna with an Ilizarov external fixator spontaneously reduced dislocations of the radial heads without the need for any additional operative intervention. All patients were satisfied with the final results.
前臂多发性遗传性外生骨疣通常形成于尺骨远端,导致尺骨生长障碍和功能障碍。多发性遗传性外生骨疣会抑制尺骨生长,导致桡骨出现内翻畸形,有时会导致桡骨头脱位、前臂旋前-旋后活动受限以及出现美容问题。
我们回顾性分析了 4 例前臂畸形伴桡骨头脱位的患者,这些患者均患有多发性遗传性外生骨疣,我们评估了切除尺骨远端骨软骨瘤和使用伊利扎洛夫外固定架逐渐延长尺骨的放射学和临床结果。
平均随访 25 个月后获得了良好的临床和放射学结果。在最近的随访中,桡骨弯曲、尺骨缩短、腕骨滑移和前臂旋前/旋后弓得到了改善。最近的随访时,桡骨关节角和肘屈伸弓几乎没有变化。
通过切除骨软骨瘤并用伊利扎洛夫外固定架逐渐延长尺骨治疗 4 例患者的 4 只前臂,可自发性地减少桡骨头脱位,无需任何其他手术干预。所有患者对最终结果均满意。