Klinik für Gynäkologie, Krankenhaus St. Elisabeth und St. Barbara Halle, Martin-Luther-Universität Halle-Wittenberg, Germany.
Klinik für Gynäkologie und Geburtshilfe, Asklepios Klinik Weißenfels-Hohenmölsen, Martin-Luther-Universität Halle-Wittenberg, Germany.
Breast Care (Basel). 2013 May;8(2):139-42. doi: 10.1159/000350778.
Poland's syndrome, a rare congenital anomaly, consists of unilateral absence of the pectoralis major muscle, ipsilateral brachysyndactyly, and occasionally associated other malformations of the anterior chest wall, mamilla, and mamma.
In the case of a 32-year-old woman, marked hypoplasia of the right breast and the right nipple, malformation of the right upper limb with brachysyndactyly and microdactyly were noted, all present since birth. This paper describes the surgical technique and possible complications of reconstruction of the chest wall deformity with a solid silicone implant and a latissimus dorsi flap. The current literature on the topic is reviewed.
The surgical method with autologous material and implants is a sufficient technique for chest wall reconstruction and gives a good long-term result in case of Poland's syndrome.
波兰氏综合征是一种罕见的先天性异常,由单侧胸大肌缺失、同侧短指并指畸形以及偶尔伴发的前胸壁、乳头和乳房的其他畸形组成。
本例为一名 32 岁女性,自出生起即存在右乳房和右乳头明显发育不良、右上肢畸形伴短指并指畸形和小指畸形。本文描述了使用固体硅胶植入物和背阔肌皮瓣矫正胸廓畸形的手术技术和可能的并发症。并对该主题的现有文献进行了回顾。
使用自体材料和植入物的手术方法是一种充分的胸廓重建技术,在波兰氏综合征的情况下可以获得良好的长期效果。