Dasgupta Malay K, Patra Chaitali, Sarkar Shatanik, Das Sabyasachi
Department of Pediatric Medicine, R. G. Kar Medical College and Hospital, Kolkata, India.
Indian Dermatol Online J. 2014 Apr;5(2):170-2. doi: 10.4103/2229-5178.131092.
Morphea is a variant of localized scleroderma in which lesions are usually limited to the skin and subcutaneous tissue. Pansclerotic morphea is a rare atrophying and sclerosing type of morphea. It can follow a comparatively benign course with spontaneous resolution of symptoms, or sometimes can lead to a variety of complications resulting in progressive disability. We report a case of Pansclerotic morphea in an 8-year-old male child involving one lower extremity with extension to the lower trunk. It was associated with deformity and hemiatrophy of that limb, leading to restriction of normal day-to-day activity. The case is being reported in view of its rare occurrence in conjunction with other rarer features.
硬斑病是局限性硬皮病的一种变体,其病变通常局限于皮肤和皮下组织。泛发性硬斑病是一种罕见的萎缩性和硬化性硬斑病类型。它可能呈现相对良性的病程,症状会自发缓解,或者有时会导致各种并发症,进而造成进行性残疾。我们报告一例8岁男性儿童的泛发性硬斑病,累及一侧下肢并延伸至下腹部。它伴有该肢体的畸形和半侧萎缩,导致正常日常活动受限。鉴于其罕见性以及其他罕见特征,现报告此病例。