内脏异位综合征患者的非心脏问题。
Non-cardiac issues in patients with heterotaxy syndrome.
作者信息
Kothari Shyam S
机构信息
Department of Cardiology, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, India.
出版信息
Ann Pediatr Cardiol. 2014 Sep;7(3):187-92. doi: 10.4103/0974-2069.140834.
Abstract
Management of complex congenital heart disease in patients with Heterotaxy syndrome (HS) has steadily improved. However, there is an insufficient appreciation of various non-cardiac issues that might impact the overall status of these patients. This article briefly reviews the implications of gastrointestinal, immunologic, genitourinary, respiratory, and central nervous system involvement in HS patients with a view to aid in their comprehensive clinical management.
摘要
异心综合征（HS）患者复杂先天性心脏病的管理已稳步改善。然而，对于可能影响这些患者整体状况的各种非心脏问题，人们的认识还不足。本文简要回顾了胃肠道、免疫、泌尿生殖、呼吸和中枢神经系统受累对HS患者的影响，以期有助于对他们进行全面的临床管理。
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