Kim Soo-Hong, Yoo Tae-Kyung, Kim Hyun-Young, Jung Sung-Eun, Park Kwi-Won
Department of Pediatric Surgery, Pusan National University Children's Yangsan Hospital, Yangsan, Korea.
Department of Pediatric Surgery, Seoul National University Children's Hospital, Seoul, Korea.
Pediatr Gastroenterol Hepatol Nutr. 2014 Sep;17(3):196-200. doi: 10.5223/pghn.2014.17.3.196. Epub 2014 Sep 30.
Co-existing pyloric submucosal masses with hypertrophic pyloric stenosis (HPS) are very rare and treating these lesions is always a problem. A 20-day-old boy presented with recurrent episodes of projectile non-bilious vomiting lasting for 5 days. HPS was suspected due to the presenting age and the symptoms. The sonography demonstrated not only circumferential wall thickening of the pylorus, but also a pyloric submucosal mass. At laparotomy, a 0.8 cm sized pyloric submucosal mass was identified along with a hypertrophied pylorus. Pyloric excision was performed due to the possibility of sustaining the symptoms and malignancy. The pathological report of the submucosal mass was ectopic pancreas. Coexisting pyloric lesions can be diagnosed along with HPS, and surgical excision, not just pyloromyotomy, should be considered in these circumstances. To the best of our knowledge, this is the first case report of pyloric ectopic pancreas and HPS to be diagnosed concurrently.
同时存在幽门黏膜下肿块与肥厚性幽门狭窄(HPS)的情况非常罕见,而治疗这些病变一直是个难题。一名20天大的男婴出现反复喷射性非胆汁性呕吐发作,持续5天。鉴于发病年龄和症状,怀疑为HPS。超声检查不仅显示幽门环周壁增厚,还发现一个幽门黏膜下肿块。剖腹探查时,发现一个0.8厘米大小的幽门黏膜下肿块以及肥厚的幽门。由于可能持续出现症状和存在恶性病变,进行了幽门切除术。黏膜下肿块的病理报告为异位胰腺。共存的幽门病变可与HPS同时诊断,在这种情况下应考虑手术切除,而不仅仅是幽门肌切开术。据我们所知,这是首例同时诊断出幽门异位胰腺和HPS的病例报告。