Gorman P H, Rigamonti D, Joslyn J N
Department of Neurology, University of Maryland Medical System, Baltimore.
Surg Neurol. 1989 Dec;32(6):459-62. doi: 10.1016/0090-3019(89)90012-8.
Intramedullary schwannomas and neurofibromas are rare tumors. Only two cases have been reported as having both an intramedullary and extramedullary component. We have managed the case of a 15-year-old girl with a schwannoma that appeared to track along the sensory nerve root into the spinal cord. The clinical presentation in this case was that of motor weakness and atrophy, sensory abnormalities, and, late in the course, pain. Magnetic resonance imaging with gadolinium enhancement was better than myelography and computed tomography at delineating the intramedullary extent of the tumor. The tumor was removed microsurgically at two operative sittings. Reports of this unusual pathology are reviewed.
髓内神经鞘瘤和神经纤维瘤是罕见的肿瘤。仅有两例报告显示肿瘤同时具有髓内和髓外成分。我们诊治了一名15岁女孩,她患有神经鞘瘤,该肿瘤似乎沿着感觉神经根延伸至脊髓。该病例的临床表现为运动无力和萎缩、感觉异常,病程后期出现疼痛。钆增强磁共振成像在描绘肿瘤的髓内范围方面优于脊髓造影和计算机断层扫描。在两次手术中通过显微手术切除了肿瘤。本文对这种不寻常的病理情况的报告进行了综述。