Saibaba Balaji, Sen Ramesh Kumar, Das Ashim, Sharma Aman
Department of Orthopaedics, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
Department of Pathology, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
Clin Orthop Surg. 2015 Dec;7(4):509-14. doi: 10.4055/cios.2015.7.4.509. Epub 2015 Nov 13.
Multicentric reticulohistiocytosis (MRH) is a rare systemic disease, which commonly manifests as muco-cutaneous papulonodules and inflammatory erosive polyarthropathy. In this research, we report the clinical manifestations and management of a rare case of MRH with destructive arthropathy of bilateral hip joints and arthritis mutilans presenting with characteristic deformities. Disabling hip arthropathy that occurs secondary to MRH can be successfully managed with bilateral total hip arthroplasty (THA). Osteopenia and acetabular bone defects must be anticipated during THA. This case is reported due to its rare occurrence and because little literature has been published regarding THA in such patients.
多中心网状组织细胞增多症(MRH)是一种罕见的系统性疾病,通常表现为黏膜皮肤丘疹结节和炎症性侵蚀性多关节病。在本研究中,我们报告了一例罕见的MRH病例的临床表现及治疗情况,该病例表现为双侧髋关节破坏性关节病和致残性关节炎,并伴有特征性畸形。继发于MRH的致残性髋关节病可通过双侧全髋关节置换术(THA)成功治疗。在进行THA时必须预见到骨质减少和髋臼骨缺损。报道该病例是因其罕见性,且关于此类患者THA的文献报道较少。