Palla Garcia José, Sampaio Rita, Peixoto Carlos
Department of Pathology, Pathological Anatomy Service, Centro Hospitalar do Porto, Largo Professor Abel Salazar, 4099-003 Porto, Portugal.
Case Rep Pathol. 2017;2017:1942595. doi: 10.1155/2017/1942595. Epub 2017 Feb 22.
The urachus is a tubular structure that connects the bladder to the allantois in the embryonic development, involuting after the third trimester. The urachus carcinoma is an extremely rare tumor that accounts for <1% of all bladder cancers. We report a case of a 46-year-old woman, with no past medical history, complaining of hematuria with 6-month duration and a physical exam and an abdominal computed topographic scan revealing an exophytic mass of 6.8 cm longer axis that grew depending on the anterior bladder wall, invading the anterior abdominal wall. Cystoscopy detected mucosal erosion. The biopsy showed structures of adenocarcinoma of enteric type. The surgical specimen showed urachus adenocarcinoma of enteric type with stage IVA in the Sheldon system and stage III in the Mayo system. This case has a 3-year follow-up without disease recurrence.
脐尿管是胚胎发育过程中连接膀胱与尿囊的管状结构,在妊娠晚期后退化。脐尿管癌是一种极其罕见的肿瘤,占所有膀胱癌的比例不到1%。我们报告一例46岁女性病例,既往无病史,主诉血尿持续6个月,体格检查及腹部计算机断层扫描显示一长轴为6.8 cm的外生性肿块,其生长依附于膀胱前壁,侵犯前腹壁。膀胱镜检查发现黏膜糜烂。活检显示为肠型腺癌结构。手术标本显示为肠型脐尿管腺癌,按照谢尔登系统分期为IVA期,按照梅奥系统分期为III期。该病例随访3年无疾病复发。