小儿烟雾病中脑-肌-软脑膜-联合血管搭桥术与脑-动脉-软脑膜-联合血管搭桥术的联合应用
Combination of Encephalo-Myo-Pial-Synangiosis and Encephalo-Arterio-Pial-Synangiosis Procedure in Pediatric Moya-Moya Disease.
作者信息
Gunawan Prastiya, Suryaningtyas Wihasto, Saharso Darto, Prasetyo Risky
机构信息
Department Of Child Health, Airlangga University, College of Medicine, Dr Soetomo Hospital, Surabaya, Indonesia.
出版信息
Ethiop J Health Sci. 2017 Mar;27(2):193-196. doi: 10.4314/ejhs.v27i2.12.
BACKGROUND
Moya-moya disease in children is a cerebrovascular disorder that may cause cerebral ischemic or hemorrhage.
CASE DETAILS
We report an 8-year-old boy that was admitted with the chief complaint of repeated sudden half left body paralyze. MRA showed acute thrombotic infarction in the right hemisphere and internal carotid artery stenosis in the form of puffs of smokes. Indirect revascularization surgical procedure with combination of Encephalo-myo-pial-synangiosis (EMS) and Encephalo-arterio-pial-synangiosis (EAS) was performed. It resulted in a good response.
CONCLUSION
Moya-moya disease can lead to permanent neurological disability if untreated. Satisfactory outcome was noted following combination surgery management with EMS and EAS.
背景
儿童烟雾病是一种可导致脑缺血或出血的脑血管疾病。
病例详情
我们报告一名8岁男孩，因反复突发左侧半身瘫痪为主诉入院。磁共振血管造影（MRA）显示右半球急性血栓性梗死，以及呈烟雾状的颈内动脉狭窄。采用脑-肌-血管融通术（EMS）和脑-动脉-血管融通术（EAS）联合的间接血运重建手术。手术效果良好。
结论
烟雾病若不治疗可导致永久性神经功能残疾。EMS和EAS联合手术治疗后取得了满意的效果。
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