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The first case of paroxysmal nocturnal hemoglobinuria and Budd-Chiari syndrome treated with complement inhibitor eculizumab in Korea.

作者信息

Kim Hyerim, Kim In-Suk, Cho Su-Hee, Lee Hyun Ji, Chang Chulhun L, Yoon Ki Tae

机构信息

Department of Laboratory Medicine, Pusan National University School of Medicine and Biomedical Research Institute Research Institute, Pusan National University Hospital, Busan, Korea.

Department of Laboratory Medicine, Pusan National University School of Medicine and Research Institute for Convergence of Biomedical Science and Technology, Yangsan, Korea.

出版信息

Blood Res. 2017 Jun;52(2):145-148. doi: 10.5045/br.2017.52.2.145. Epub 2017 Jun 22.

DOI:10.5045/br.2017.52.2.145

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5503897/

Abstract

摘要

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fcf1/5503897/e5900c77b763/br-52-145-g001.jpg

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1

Incidence, prevalence and complications of Budd-Chiari syndrome in South Korea: a nationwide, population-based study.

Liver Int. 2016 Jul;36(7):1067-73. doi: 10.1111/liv.13008. Epub 2015 Dec 6.

2

Treatment of a patient with classical paroxysmal nocturnal hemoglobinuria and Budd-Chiari syndrome, with complement inhibitor eculizumab: Case Report.

Hippokratia. 2013 Jan;17(1):81-4.

3

Clinical signs and symptoms associated with increased risk for thrombosis in patients with paroxysmal nocturnal hemoglobinuria from a Korean Registry.

Int J Hematol. 2013 Jun;97(6):749-57. doi: 10.1007/s12185-013-1346-4. Epub 2013 May 1.

4

Eculizumab in paroxysmal nocturnal hemoglobinuria with Budd-Chiari syndrome progressing despite anticoagulation.

Exp Hematol Oncol. 2012 Sep 6;1(1):26. doi: 10.1186/2162-3619-1-26.

5

Guidelines for the diagnosis and monitoring of paroxysmal nocturnal hemoglobinuria and related disorders by flow cytometry.

Cytometry B Clin Cytom. 2010 Jul;78(4):211-30. doi: 10.1002/cyto.b.20525.

6

Paroxysmal nocturnal hemoglobinuria in Budd-Chiari syndrome: findings from a cohort study.

J Hepatol. 2009 Oct;51(4):696-706. doi: 10.1016/j.jhep.2009.06.019. Epub 2009 Jul 23.

7

Successful liver transplantation for Budd-Chiari syndrome in a patient with paroxysmal nocturnal hemoglobinuria treated with the anti-complement antibody eculizumab.

Liver Transpl. 2009 May;15(5):540-3. doi: 10.1002/lt.21714.

8

Effect of the complement inhibitor eculizumab on thromboembolism in patients with paroxysmal nocturnal hemoglobinuria.

Blood. 2007 Dec 1;110(12):4123-8. doi: 10.1182/blood-2007-06-095646. Epub 2007 Aug 16.

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Recent advances in the diagnosis, monitoring, and management of patients with paroxysmal nocturnal hemoglobinuria.

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Myeloproliferative disease in the pathogenesis and survival of Budd-Chiari syndrome.

Haematologica. 2006 Dec;91(12):1712-3.