Bhandohal Janpreet Singh, Mirza Taimur
Department of Internal Medicine, New York Medical College at Metropolitan Hospital Center, 1901 First avenue, New York, NY 10029, United States.
Am J Emerg Med. 2017 Oct;35(10):1581.e1-1581.e2. doi: 10.1016/j.ajem.2017.07.021. Epub 2017 Jul 5.
Idiopathic Intracranial Hypertension (IIH) is a syndrome seen predominantly in obese women of reproductive age group, characterized by signs and symptoms of increased intracranial pressure due to an unknown cause. Some individuals have a more malignant form of disease called fulminant idiopathic intracranial hypertension with rapid worsening of symptoms over days. We report a case of 33year-old obese female (BMI 36.9) who presented with a severe headache and blurred vision for one week, found to have idiopathic intracranial hypertension with rapid worsening of symptoms suggestive of a fulminant course of disease. She was managed with prompt surgical intervention. In patients with fulminant idiopathic intracranial hypertension, surgery such as cerebrospinal fluid shunting or optic nerve sheath fenestration should not be delayed to prevent vision loss.
特发性颅内高压(IIH)是一种主要见于育龄肥胖女性的综合征,其特征是由未知原因导致颅内压升高的体征和症状。一些个体患有更恶性的疾病形式,称为暴发性特发性颅内高压,症状在数天内迅速恶化。我们报告一例33岁肥胖女性(BMI 36.9),她出现严重头痛和视力模糊一周,被诊断为特发性颅内高压,症状迅速恶化,提示疾病呈暴发性病程。她接受了及时的手术干预。对于暴发性特发性颅内高压患者,不应延迟进行脑脊液分流或视神经鞘开窗等手术,以防止视力丧失。