Department of Radiology, Chung-Ang University Hospital, Chung-Ang University College of Medicine, Seoul, Korea.
Department of Pathology, Soonchunhyang University Cheonan Hospital, Soonchunhyang University College of Medicine, Cheonan, Korea.
J Korean Med Sci. 2017 Dec;32(12):2079-2084. doi: 10.3346/jkms.2017.32.12.2079.
Solid pseudopapillary tumor (SPT) is a low grade malignant tumor in the pancreas, and extrapancreatic SPT is extremely rare. We report a case of a 61-year-old woman who complained abdominal pain with diffuse tenderness. She was diagnosed with extrapancreatic SPT with extensive peritoneal dissemination and hepatic metastases. Although a few cases have reported imaging findings of extrapancreatic SPT, there have been no reports of extrapancreatic SPT with aggressive tumor behavior and dismal prognosis. Although imaging features closely resembled those of classical pancreatic SPTs, malignant transformation of extrapancreatic SPT should be considered when focal discontinuity of the tumor capsule with ill-defined margin and invasion of adjacent structures were identified.
实性假乳头状瘤(SPT)是一种低度恶性胰腺肿瘤,胰腺外 SPT 极为罕见。我们报告了一例 61 岁女性,她主诉腹痛伴弥漫性压痛。她被诊断为胰腺外 SPT,广泛腹膜播散和肝转移。虽然少数病例报道了胰腺外 SPT 的影像学表现,但尚无侵袭性肿瘤行为和预后不良的胰腺外 SPT 报道。尽管影像学特征与经典胰腺 SPT 非常相似,但当发现肿瘤包膜局灶性不连续、边界不清和邻近结构侵犯时,应考虑胰腺外 SPT 的恶性转化。