眼眶孤立性朗格汉斯组织细胞增多症：病例报告及文献复习

Solitary Langerhans histiocytosis of the orbit: case report and review of the literature.

作者信息

Şovrea Alina Simona, Bartoş Dana Monica, Bartoş Adrian, Dronca Eleonora, Szabo Bianca Aurora

机构信息

Department of Molecular Sciences, "Iuliu Hatieganu" University of Medicine and Pharmacy, Cluj-Napoca, Romania;

出版信息

Rom J Morphol Embryol. 2017;58(4):1589-1595.

PMID:29556661

Abstract

Langerhans cell histiocytosis (LCH), previously known as "histiocytosis X", is a clinical entity characterized by abnormal proliferation of Langerhans cells, which exert a mass effect. Orbital involvement due to LCH is rare as a unifocal disease, seldom occurring outside the pediatric population. We report a case of a 21-year-old man with solitary LCH of the orbit depicted by magnetic resonance imaging (MRI) and diagnosed by histopathological examination.

摘要

朗格汉斯细胞组织细胞增多症（LCH），以前称为“组织细胞增多症X”，是一种以朗格汉斯细胞异常增殖并产生占位效应为特征的临床病症。作为一种单灶性疾病，LCH累及眼眶的情况罕见，很少发生在儿童群体之外。我们报告一例21岁男性眼眶孤立性LCH病例，通过磁共振成像（MRI）显示并经组织病理学检查确诊。