Cha Seul Gi, Kim Gi Beom, Noh Chung Il, Kim Woong Han
Department of Pediatrics, Seoul National University Children's Hospital, Seoul, South Korea.
Department of Thoracic and Cardiovascular Surgery, Seoul National University Children's Hospital, Seoul, South Korea.
Interact Cardiovasc Thorac Surg. 2018 Oct 1;27(4):629-631. doi: 10.1093/icvts/ivy118.
Managing protein-losing enteropathy after Fontan surgery is challenging. We report a case of protein-losing enteropathy associated with Fontan circulation in a 14-year-old boy. He was treated medically for 2 years, without improvement until Fontan takedown and pulsatile bidirectional cavopulmonary shunting were performed.
在Fontan手术后管理蛋白丢失性肠病具有挑战性。我们报告了一例14岁男孩与Fontan循环相关的蛋白丢失性肠病病例。他接受了2年的药物治疗,但没有改善,直到进行了Fontan拆除和搏动性双向腔肺分流术。