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三叉戟征在长节段横贯性脊髓炎中的诊断价值优于水通道蛋白 4 免疫球蛋白 G ELISA。

Trident sign trumps Aquaporin-4-IgG ELISA in diagnostic value in a case of longitudinally extensive transverse myelitis.

机构信息

Departments of Neurology, Mayo Clinic, Rochester, MN, USA.

Departments of Neurology, Mayo Clinic, Rochester, MN, USA; Laboratory Medicine and Pathology, Mayo Clinic, Rochester, MN, USA.

出版信息

Mult Scler Relat Disord. 2018 Jul;23:7-8. doi: 10.1016/j.msard.2018.04.012. Epub 2018 Apr 21.

DOI:10.1016/j.msard.2018.04.012
PMID:29709797
Abstract

Longitudinally-extensive T2-hyperintense spinal cord lesions (≥3 vertebral segments) are associated with neuromyelitis optical spectrum disorder but occur with other disorders including spinal cord sarcoidosis. When linear dorsal subpial enhancement is accompanied by central cord/canal enhancement the axial post-gadolinium sequences may reveal a "trident" pattern that has previously been shown to be strongly suggestive of spinal cord sarcoidosis. We report a case in which the patient was initially diagnosed with neuromyelitis optical spectrum disorder, but where the "trident" sign ultimately led to the correct diagnosis of spinal cord sarcoidosis.

摘要

纵向广泛的 T2 高信号脊髓病变(≥3 个椎体节段)与视神经脊髓炎谱系疾病相关,但也可发生于其他疾病,包括脊髓结节病。当线性背侧皮质下增强伴有中央脊髓/管增强时,轴向钆后序列可能显示出以前被强烈提示为脊髓结节病的“三叉戟”模式。我们报告了一例患者最初被诊断为视神经脊髓炎谱系疾病,但“三叉戟”征最终导致了正确的脊髓结节病诊断。

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