Pelit Eyyüp Sabri, Erol Bülent, Zenginkinet Tülay, Çaşkurlu Turhan
Department of Urology, Medeniyet University Göztepe Training and Research Hospital, İstanbul, Turkey.
Department of Pathology, Medeniyet University Göztepe Training and Research Hospital, İstanbul, Turkey.
Turk J Urol. 2018 Jul;44(4):370-372. doi: 10.5152/tud.2017.69345.
Testicular sex cord-stromal tumors constitute a small portion of all types of testicular tumors. Only 1% of these tumors are pure Sertoli cell tumors. Sertoli cell tumors have three identified subgroups: large-cell calcifying (LCCSCT), sclerosing Sertoli cell and general type. Up to 40% of LCCSCT are associated with the genetic syndromes like Carney complex, Peutz-Jeghers syndrome. These lesions are usually benign, only 17% of the cases show malignant behaviour. Herein, we report a case of unilateral LCCSCT in a 37 year-old man without any hormonal symptoms or inherited diseases which was succesfully treated with testis-sparing surgery.
睾丸性索间质肿瘤在所有类型的睾丸肿瘤中占比很小。这些肿瘤中只有1%是纯支持细胞瘤。支持细胞瘤有三个已确定的亚组:大细胞钙化型(LCCSCT)、硬化性支持细胞型和普通型。高达40%的LCCSCT与卡尼综合征、黑斑息肉综合征等遗传综合征相关。这些病变通常是良性的,只有17%的病例表现出恶性行为。在此,我们报告一例37岁男性单侧LCCSCT病例,该患者无任何激素症状或遗传性疾病,经保留睾丸手术成功治疗。