Cruz E Silva Vera, Luís Ana, Mora Féria Rita, Marques Luís, Chorão Martinha, Reizinho Carla, Graça Joana
Department of Neuroradiology, Egas Moniz Hospital, Lisbon, Portugal.
Department of Neurosurgery, Egas Moniz Hospital, Lisbon, Portugal.
BJR Case Rep. 2016 Nov 10;3(2):20160082. doi: 10.1259/bjrcr.20160082. eCollection 2017.
Spontaneous transsphenoidal meningoencephalcele is a rare entity, even rarer through the Sternberg's canal, a congenital defect on the lateral wall of the sphenoid sinus. We report such a case in an obese 52-year-old female with spontaneous cerebrospinal fluid (CSF) rhinorrhoea and recurrent meningitis. Brain CT, MRI and CT cisternography were performed. Surgical correction and short-term follow-up were recorded. CT scan showed a defect on the lateral wall of the right sphenoid sinus filled with a soft tissue mass extending to the nasal cavity. MRI scan revealed brain parenchyma from the right temporal lobe herniated through the sphenoid bone defect. CT cisternography showed 270 mmHO opening pressure and confirmed the CSF leakage. Surgical correction was performed with resolution of the symptoms. MRI and CT are complementary modalities for evaluating this entity, the first being the method of choice for meningoencephalcele diagnosis although bone defects are best depicted on CT scan. CT cisternography identifies the specific site of leak and confirms benign intracranial hypertension, consistently reported in meningoencephaloceles. Obesity and benign intracranial hypertension have been reported as a combined mechanism allegedly contributing to meningoencephaloceles through congenital skull base defects, by increasing intraabdominal pressure thus decreasing venous return, with augmented intracranial pressure and subsequent reduced absorption of the CSF.
自发性经蝶窦脑膜脑膨出是一种罕见的疾病,经蝶窦外侧壁先天性缺损的施特恩贝格管(Sternberg's canal)发生者更为罕见。我们报告了一例52岁肥胖女性患者,患有自发性脑脊液鼻漏和复发性脑膜炎。进行了脑部CT、MRI和CT脑池造影检查,并记录了手术矫正及短期随访情况。CT扫描显示右侧蝶窦外侧壁有一缺损,内有一软组织肿块延伸至鼻腔。MRI扫描显示右颞叶脑实质通过蝶骨缺损处疝出。CT脑池造影显示开放压为270mmH₂O,并证实存在脑脊液漏。手术矫正后症状得以缓解。MRI和CT是评估该疾病的互补性检查方法,虽然CT扫描能更好地显示骨缺损,但MRI是诊断脑膜脑膨出的首选方法。CT脑池造影可确定漏出的具体部位,并证实脑膜脑膨出中一直报道的良性颅内高压。肥胖和良性颅内高压被认为是一种联合机制,据称通过先天性颅底缺损导致脑膜脑膨出,即通过增加腹腔内压力从而减少静脉回流,导致颅内压升高,进而使脑脊液吸收减少。