Jaramillo Carolina, Nyquist Christina, Riggan Kirsten A, Egginton Jason, Phelan Sean, Allyse Megan
Mayo Clinic, Rochester, MN, USA.
Clin Pediatr (Phila). 2019 Mar;58(3):336-342. doi: 10.1177/0009922818817310. Epub 2018 Dec 5.
Increased prenatal diagnoses of sex chromosome aneuploidies (SCAs) amid limited knowledge of their prognoses heighten the need to understand how families contend with the implications of an SCA. To explore the experiences of parents and individuals who received a genetic diagnosis of an SCA (excluding Turner syndrome), we conducted semistructured qualitative telephone interviews with 43 participants affected by these conditions. Parents (n = 35) and individuals (n = 8) expressed almost unanimous interest in more optimistic portrayals of their condition from their providers, even when the prognosis is uncertain. While some participants reported success in receiving accurate information from their provider and identifying supportive resources, numerous families received outdated or misleading information about their condition and lacked direction in accessing follow-up care and support. Parents desire greater coordination of their child's medical care and access to care that approaches an SCA holistically. Opportunities remain to improve the diagnosis and care of individuals with SCAs.
在对性染色体非整倍体(SCA)预后了解有限的情况下,产前对其诊断的增加凸显了了解家庭如何应对SCA影响的必要性。为了探究接受SCA基因诊断(不包括特纳综合征)的父母和个人的经历,我们对43名受这些病症影响的参与者进行了半结构化定性电话访谈。父母(n = 35)和个人(n = 8)几乎一致表示,即使预后不确定,他们也希望医疗服务提供者能对他们的病情有更乐观的描述。虽然一些参与者报告说成功从医疗服务提供者那里获得了准确信息并找到了支持资源,但许多家庭收到的是关于他们病情的过时或误导性信息,并且在获得后续护理和支持方面缺乏指导。父母希望孩子的医疗护理能有更好的协调,并能获得全面处理SCA的护理。改善SCA患者的诊断和护理仍有机会。