Farat Joyce Godoy, Queiroz Marjorie Fornazier Nascimento, Lottelli Antonio Carlos
Department of Ophthalmology, Otorhinolaryngology and Head and Neck Surgery, Faculdade de Medicina de Botucatu, Universidade Estadual Paulista "Julio de Mesquita Filho", Botucatu, SP, Brazil.
Arq Bras Oftalmol. 2019 Jan-Feb;82(1):62-64. doi: 10.5935/0004-2749.20190012.
We report the case of a 4-year-old boy with Marfan syndrome whose parents reported he had had low visual acuity since birth. On examination, there was microspherophakia and a small subluxation of the lens. The objective refraction was -23.75 - 2.75 x 70 in the right eye and -25.50 -3.50 x 90 in the left eye. Since the microspherophakia and the high myopia severely affected the boy's quality of life, clear lens extraction, anterior vitrectomy, posterior surgical capsulotomy via the pars plana, and intraocular lens implantation were performed. Two years postoperatively, the patient had centered intraocular lenses and a corrected visual acuity of 20/30 in both eyes. The child was satisfied with his vision and was able to study and perform daily activities without visual limitations.
我们报告了一名患有马凡综合征的4岁男孩的病例,其父母称他自出生以来视力就很低。检查发现有小晶状体和晶状体轻度半脱位。右眼客观验光结果为-23.75 - 2.75×70,左眼为-25.50 - 3.50×90。由于小晶状体和高度近视严重影响了男孩的生活质量,因此进行了透明晶状体摘除术、前部玻璃体切除术、经睫状体扁平部的后部手术囊切开术以及人工晶状体植入术。术后两年,患者的人工晶状体居中,双眼矫正视力为20/30。孩子对自己的视力很满意,能够在没有视力限制的情况下学习和进行日常活动。