非典型肺泡蛋白沉积症。

Atypical alveolar proteinosis.

作者信息

Rajaonarison Ny Ony Narindra Lova Hasina, Andrianah Emmylou Gabrielle, Ranaivomanana Volahasina Francine, Tomboravo Christian, Ranoharison Hasina Dina, Bruneton Jean Noel, Ahmad Ahmad

机构信息

Department of Medical Imaging Services of JRA Hospital, Antananarivo, Madagascar.

Department of Medical Biology, Anatomopathological Services of JRA Hospital, Antananarivo, Madagascar.

出版信息

Indian J Radiol Imaging. 2018 Oct-Dec;28(4):439-441. doi: 10.4103/ijri.IJRI_170_18.

DOI:10.4103/ijri.IJRI_170_18

PMID:30662206

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6319097/

Abstract

Alveolar proteinosis is a rare pulmonary disease characterized by intra-alveolar accumulation of surfactant composed of lipoproteinaceous material, related to a lack of surfactant resorption by alveolar macrophages. Crazy paving pattern is characteristic, but not specific. The multinodular forms of this affection remain exceptional.

摘要

肺泡蛋白沉积症是一种罕见的肺部疾病，其特征为肺泡内积聚由脂蛋白物质构成的表面活性物质，这与肺泡巨噬细胞对表面活性物质的再吸收缺乏有关。铺路石样表现具有特征性，但并非特异性表现。这种疾病的多结节形式仍然罕见。