Belzile Eugénie, Funaro Deana, Powell Julie
Division of Dermatology, CHU Sainte-Justine, University of Montreal, Montreal, Quebec, Canada.
Pediatr Dermatol. 2019 May;36(3):349-351. doi: 10.1111/pde.13771. Epub 2019 Feb 14.
Localized vulvar bullous pemphigoid of childhood is an excessively rare variant of bullous pemphigoid and affects almost exclusively young girls of 7-12 years of age. In contrast to adult-onset bullous pemphigoid, a prompt response to potent topical corticosteroids is observed in the majority of cases, with a favorable prognosis and rare relapses. We report the case of a 7-year-old girl who presented with this condition. Our case reinforces the recognition of this rare subtype of childhood bullous pemphigoid as a distinct entity and enlightens the importance of performing a cutaneous biopsy when clinically indicated.
儿童局限性外阴大疱性类天疱疮是大疱性类天疱疮一种极其罕见的变异类型,几乎仅影响7至12岁的年轻女孩。与成人发病的大疱性类天疱疮不同,大多数病例对强效外用皮质类固醇激素反应迅速,预后良好且复发罕见。我们报告了一名患有这种疾病的7岁女孩的病例。我们的病例强化了对这种罕见的儿童大疱性类天疱疮亚型作为一种独特疾病实体的认识,并突显了在临床指征明确时进行皮肤活检的重要性。