Department of Laboratory Medicine and Pathobiology, University of Toronto, Toronto, M5S 1A8, Canada.
Program in Developmental and Stem Cell Biology, The Hospital for Sick Children, 686 Bay Street, Toronto, M5G 0A4, Canada.
Pediatr Nephrol. 2020 May;35(5):725-731. doi: 10.1007/s00467-019-04240-8. Epub 2019 Mar 28.
Aberrant hedgehog (Hh) signaling during embryogenesis results in various severe congenital abnormalities, including renal malformations. The molecular mechanisms that underlie congenital renal malformations remain poorly understood. Here, we review the current understanding of the lineage-specific roles of Hh signaling during renal morphogenesis and how aberrant Hh signaling during embryonic kidney development contributes to renal malformation.
胚胎发育过程中 Hedgehog(Hh)信号通路的异常会导致各种严重的先天性异常,包括肾脏畸形。导致先天性肾脏畸形的分子机制仍知之甚少。本文综述了 Hh 信号在肾脏形态发生过程中对谱系特异性的作用的最新认识,以及胚胎肾脏发育过程中异常的 Hh 信号如何导致肾脏畸形。