由免疫球蛋白G4相关疾病（IgG4-RD）引起的巨大尿道周围肿块导致的女性尿潴留。
Female urinary retention from a huge periurethral mass caused by immunoglobulin G4-related disease (IgG4-RD).
作者信息
Sangsoad Phadungsak, Ramart Patkawat, Korpraphong Pornpim, Rerkpichaisuth Vilasinee, Pradniwat Kanapon, Treetipsatit Jitsupa
机构信息
Division of Urology, Department of Surgery, Faculty of Medicine, Siriraj Hospital, Mahidol University, 12th Fl. Syamindra Bldg., Siriraj Hospital, Prannok Rd., Bangkok-Noi, Bangkok, 10700, Thailand.
Division of Diagnostic Radiology, Department of Radiology, Faculty of Medicine, Siriraj Hospital, Mahidol University, Bangkok, Thailand.
出版信息
Urol Case Rep. 2019 Jan 31;24:100844. doi: 10.1016/j.eucr.2019.100844. eCollection 2019 May.
Immunoglobulin G4-related disease is a systemic disease, recognized as extensive T-lymphocyte and IgG4-positive plasma cells. It can present as inflammatory pseudotumor in various organs. A female 75 years old, diagnosed IgG4-related autoimmune pancreatitis, presented with urinary retention. Pelvic examination showed well-defined, soft tissue mass, bulging from anterior vaginal wall. MRI pelvis demonstrated a huge periurethral mass, size 6.2 × 4.4 × 4.2 cm, encasing the urethra, extending from bladder neck to distal urethra, and mimicking the prostate gland. Tissue biopsy showed compatible with IgG4-related disease. Immunosuppresive drugs were given for few months and the patient could void normally.
免疫球蛋白G4相关性疾病是一种全身性疾病，其特征为广泛的T淋巴细胞和IgG4阳性浆细胞。它可在各个器官表现为炎性假瘤。一名75岁女性，诊断为IgG4相关性自身免疫性胰腺炎，出现尿潴留。盆腔检查发现界限清楚的软组织肿块，从阴道前壁膨出。盆腔磁共振成像显示一个巨大的尿道周围肿块，大小为6.2×4.4×4.2厘米，包绕尿道，从膀胱颈延伸至尿道远端，类似前列腺。组织活检显示符合IgG4相关性疾病。给予免疫抑制药物治疗数月后，患者能够正常排尿。
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