Roncall Bhim Raju, Bellapukonda Snigdha, Mohanty Chitta Ranjan
Anesthesia, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India.
Trauma and Emergency, All India Institute of Medical Science, Bhuvaneshwar, Odisha, India.
BMJ Case Rep. 2019 Jul 8;12(7):e230394. doi: 10.1136/bcr-2019-230394.
Diencephalic syndrome is one of the rare causes of failure to thrive in infants and young children. It is caused by a tumour in diencephalon (thalamus and hypothalamus), characterised by profound emaciation with uniform loss of body weight despite normal or slightly decreased appetite, locomotor hyperactivity, euphoria and visual symptoms. Anaesthetic considerations due to decreased body fat include positioning to avoid pressure necrosis, measures to avoid hypothermia, proper drug dosing, treating electrolyte imbalances and delayed recovery. We report successful anaesthetic management of a child with diencephalic syndrome scheduled for an endoscopic biopsy of suprasellar space occupying lesion under general anaesthesia.
间脑综合征是婴幼儿生长发育迟缓的罕见原因之一。它由间脑(丘脑和下丘脑)肿瘤引起,特征为尽管食欲正常或略有下降,但体重却均匀减轻导致严重消瘦、运动活动亢进、欣快感和视觉症状。由于体脂减少,麻醉时需考虑避免受压坏死的体位摆放、预防体温过低的措施、正确的药物剂量、治疗电解质失衡以及恢复延迟等问题。我们报告了一例间脑综合征患儿在全身麻醉下接受鞍上占位性病变内镜活检的麻醉成功管理案例。