三级医院中肛门直肠畸形伴食管闭锁的 5 年经验。
Five-year experience of anorectal malformation with oesophageal atresia in tertiary care hospital.
机构信息
Department of Paediatric Surgery, IMS, BHU, Varanasi, Uttar Pradesh, India.
出版信息
Afr J Paediatr Surg. 2020 Jul-Dec;17(3 & 4):49-53. doi: 10.4103/ajps.AJPS_54_17.
AIM
We had done this study for TEF with Anorectal malformation and TEF with no Anorectal malformation in terms of age, sex, surgical outcomes and mortality.
MATERIALS AND METHODS
This was a retrospective review of cases with clinical data (from April 2012 to April 2017). The participants of this study were 236 patients who had been diagnosed and managed for ARM. Among these patients, 25 patients associated with EA were selected as the subject patient group.
RESULTS
The incidence of tracheoesophageal fistula with ARM was 11.1%. The study has more male preponderance. All cases are of Type c except two cases of Type a. According to the classifications of ARMs, there were two cases with rectourethral fistula and eight cases with rectoperineal fistula and covered anus in the males. In females, there was a varied distribution of seven cases. There was one case (4%) presenting as a part of the Vertebral anorectal malformation cardiac tracheoesophageal renal and limb anomalies (VACTERL) association, which is the representative example of a complex anomaly. Most of the cases died due to cardiac problem and pneumonitis (due to delayed presentation).
CONCLUSION
The study concludes the experience of EA (±fistulae) with ARM, their distribution, incidence and outcome of the tertiary care centre.
目的
我们对伴有和不伴有肛门直肠畸形的食管气管瘘（TEF）患者进行了年龄、性别、手术结果和死亡率方面的研究。
材料和方法
这是一项回顾性研究，纳入了 2012 年 4 月至 2017 年 4 月期间具有临床数据的 236 例 ARM 患者，其中 25 例 EA 患者被选为本研究的病例组。
结果
ARM 伴发 TEF 的发病率为 11.1%。研究中男性患者多于女性。所有病例均为 c 型，仅有 2 例为 a 型。根据 ARM 的分类，男性中有 2 例直肠尿道瘘和 8 例直肠会阴瘘伴肛门闭锁，女性中则有 7 例分布各不相同。有 1 例（4%）为脊柱肛门直肠畸形伴心脏、气管食管肾和肢体异常（VACTERL）综合征的一部分，这是一种复杂畸形的典型代表。大多数病例死于心脏问题和肺炎（由于延迟就诊）。
结论
本研究总结了三级医疗中心的 EA（伴或不伴瘘管）、其分布、发病率和结果的经验。
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