Ruaro Barbara, Santiago Tania, Hughes Michael, Lepri Gemma, Poillucci Gabriele, Baratella Elisa, Salton Francesco, Confalonieri Marco
Unit of Pulmonology, University Hospital of Trieste, Trieste, Italy.
Department of Rheumatology, Centro Hospitalare Universitário de Coimbra, Coimbra, Portugal.
Open Access Rheumatol. 2021 Apr 28;13:79-91. doi: 10.2147/OARRR.S282612. eCollection 2021.
Systemic sclerosis (SSc), an autoimmune connective tissue disease, characterized by skin fibrosis, increased dermal thickness and microvascular involvement. Fibroblasts and myofibroblasts deposit excessive amounts of collagenous and non-collagenous extracellular matrix components in the skin. This leads to microvascular abnormalities and Raynaud's phenomenon, with painful digital ulcers (DU) at the fingertips adding to patient discomfort. The skin involvement and severity in SSc was evaluated by the Modified Rodnan skin score (mRSS). Although high-frequency ultrasound (HUS) has been widely researched in the study of skin thickness and DU in SSc, its adoption into clinical practice is not yet common. However, novel insights into the still relatively unknown disease pathogenesis in SSc and its evaluation may be provided by HUS, including early (pre-clinical) skin involvement. It may also be useful in both the evaluation and follow-up of DU. Indeed, it is a non-invasive, safe, inexpensive and reproducible method able to assess not only SSc patients' cutaneous structural changes, but also their vascular system changes. Moreover, several recent studies have reported that elastosonography (ES) is of use when investigating skin involvement in systemic sclerosis. This review aims at providing information as to role HUS and ES play in research advancements and the clinical perspectives in the evaluation of skin thickness and DU in SSc patients.
系统性硬化症(SSc)是一种自身免疫性结缔组织疾病,其特征为皮肤纤维化、真皮厚度增加和微血管受累。成纤维细胞和肌成纤维细胞在皮肤中沉积过量的胶原和非胶原细胞外基质成分。这会导致微血管异常和雷诺现象,指尖疼痛的指端溃疡(DU)会增加患者的不适感。SSc的皮肤受累情况和严重程度通过改良Rodnan皮肤评分(mRSS)进行评估。尽管高频超声(HUS)在SSc的皮肤厚度和DU研究中已得到广泛研究,但其在临床实践中的应用尚不普遍。然而,HUS可能会为SSc中仍相对未知的疾病发病机制及其评估提供新的见解,包括早期(临床前)皮肤受累情况。它在DU的评估和随访中也可能有用。事实上,它是一种非侵入性、安全、廉价且可重复的方法,不仅能够评估SSc患者的皮肤结构变化,还能评估其血管系统变化。此外,最近的几项研究报告称,弹性超声检查(ES)在研究系统性硬化症的皮肤受累情况时是有用的。本综述旨在提供有关HUS和ES在研究进展以及评估SSc患者皮肤厚度和DU的临床前景中所起作用的信息。